MCCC2 polyclonal antibody (A01)
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More Files
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Western Blot (Cell lysate)
MCCC2 polyclonal antibody (A01), Lot # 051212JC01 Western Blot analysis of MCCC2 expression in MES-SA/Dx5 ( Cat # L021V1 ).
Western Blot detection against Immunogen (37.99 KDa) .
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Specification
Product Description
Mouse polyclonal antibody raised against a partial recombinant MCCC2.
Immunogen
MCCC2 (NP_071415, 456 a.a. ~ 563 a.a) partial recombinant protein with GST tag.
Sequence
AYSPRFLYIWPNARISVMGGEQAANVLATITKDQRAREGKQFSSADEAALKEPIIKKFEEEGNPYYSSARVWDDGIIDPADTRLVLGLSFSAALNAPIEKTDFGIFRM
Host
Mouse
Reactivity
Human
Interspecies Antigen Sequence
Mouse (88); Rat (88)
Quality Control Testing
Antibody Reactive Against Recombinant Protein.
Western Blot detection against Immunogen (37.99 KDa) .
Storage Buffer
50 % glycerol
Storage Instruction
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
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Applications
Western Blot (Cell lysate)
MCCC2 polyclonal antibody (A01), Lot # 051212JC01 Western Blot analysis of MCCC2 expression in MES-SA/Dx5 ( Cat # L021V1 ).Western Blot (Recombinant protein)
ELISA
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Gene Info — MCCC2
Entrez GeneID
64087GeneBank Accession#
NM_022132Protein Accession#
NP_071415Gene Name
MCCC2
Gene Alias
MCCB
Gene Description
methylcrotonoyl-Coenzyme A carboxylase 2 (beta)
Gene Ontology
HyperlinkGene Summary
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq
Other Designations
biotin carboxylase|non-biotin containing subunit of 3-methylcrotonyl-CoA carboxylase
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Interactome
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Pathway
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Disease
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Publication Reference
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Cryptic Exon Activation by Disruption of Exon Splice Enhancer: NOVEL MECHANISM CAUSING 3-METHYLCROTONYL-CoA CARBOXYLASE DEFICIENCY.
Stucki M, Suormala T, Fowler B, Valle D, Baumgartner MR.
The Journal of Biological Chemistry 2009 Oct; 284(42):28953.
Application：WB, Human, Fibroblast cells.
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Cryptic Exon Activation by Disruption of Exon Splice Enhancer: NOVEL MECHANISM CAUSING 3-METHYLCROTONYL-CoA CARBOXYLASE DEFICIENCY.
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