PEX7 polyclonal antibody (A01)

Catalog # H00005191-A01

Size

Price

Stock

Quantity

Size:50 uL
Price: USD $ 243.00
Stock:
order now, ship in 3 months
abnova-minus
abnova-plus

* The price is valid only in USA. Please select country.

Contact Info
  • +1-909-264-1399
    +1-909-992-0619
    Toll Free : +1-877-853-6098
  • +1-909-992-3401
Images
Western Blot (Cell lysate)
Application

Western Blot (Cell lysate)

PEX7 polyclonal antibody (A01), Lot # 051122JC01. Western Blot analysis of PEX7 expression in Raw 264.7.

QC Test

Western Blot detection against Immunogen (36.89 KDa) .

  • Specification

    Product Description

    Mouse polyclonal antibody raised against a partial recombinant PEX7.

    Immunogen

    PEX7 (NP_000279, 2 a.a. ~ 99 a.a) partial recombinant protein with GST tag.

    Sequence

    SAVCGGAARMLRTPGRHGYAAEFSPYLPGRLACATAQHYGIAGCGTLLILDPDEAGLRLFRSFDWNDGLFDVTWSENNEHVLITCSGDGSLQLWDTAK

    Host

    Mouse

    Reactivity

    Human, Mouse

    Interspecies Antigen Sequence

    Mouse (88); Rat (87)

    Quality Control Testing

    Antibody Reactive Against Recombinant Protein.

    Western Blot detection against Immunogen (36.89 KDa) .

    Storage Buffer

    50 % glycerol

    Storage Instruction

    Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

  • Applications

    Western Blot (Cell lysate)

    PEX7 polyclonal antibody (A01), Lot # 051122JC01. Western Blot analysis of PEX7 expression in Raw 264.7.

    Western Blot (Recombinant protein)

    ELISA

  • Gene Info — PEX7

    Entrez GeneID

    5191

    GeneBank Accession#

    NM_000288

    Protein Accession#

    NP_000279

    Gene Name

    PEX7

    Gene Alias

    PTS2R, RCDP1, RD

    Gene Description

    peroxisomal biogenesis factor 7

    Omim ID

    215100 266500 601757

    Gene Ontology

    Hyperlink

    Gene Summary

    This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq

    Other Designations

    OTTHUMP00000017277|peroxin-7|peroxisomal PTS2 receptor|peroxisome targeting signal 2 receptor

  • Interactome
  • Disease
Contact Info
  • +1-909-264-1399
    +1-909-992-0619
    Toll Free : +1-877-853-6098
  • +1-909-992-3401
4 Products to Compare
Remove All