PEX7 polyclonal antibody (A01)
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More Files
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Specification
Product Description
Mouse polyclonal antibody raised against a partial recombinant PEX7.
Immunogen
PEX7 (NP_000279, 2 a.a. ~ 99 a.a) partial recombinant protein with GST tag.
Sequence
SAVCGGAARMLRTPGRHGYAAEFSPYLPGRLACATAQHYGIAGCGTLLILDPDEAGLRLFRSFDWNDGLFDVTWSENNEHVLITCSGDGSLQLWDTAK
Host
Mouse
Reactivity
Human, Mouse
Interspecies Antigen Sequence
Mouse (88); Rat (87)
Quality Control Testing
Antibody Reactive Against Recombinant Protein.
Western Blot detection against Immunogen (36.89 KDa) .
Storage Buffer
50 % glycerol
Storage Instruction
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
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Applications
Western Blot (Cell lysate)
PEX7 polyclonal antibody (A01), Lot # 051122JC01. Western Blot analysis of PEX7 expression in Raw 264.7.Western Blot (Recombinant protein)
ELISA
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Gene Info — PEX7
Entrez GeneID
5191GeneBank Accession#
NM_000288Protein Accession#
NP_000279Gene Name
PEX7
Gene Alias
PTS2R, RCDP1, RD
Gene Description
peroxisomal biogenesis factor 7
Gene Ontology
HyperlinkGene Summary
This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq
Other Designations
OTTHUMP00000017277|peroxin-7|peroxisomal PTS2 receptor|peroxisome targeting signal 2 receptor
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Interactome
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Disease
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