GUSB purified MaxPab mouse polyclonal antibody (B01P)

Catalog # H00002990-B01P

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Size:50 ug
Price: USD $ 335.00
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Contact Info
  • +1-909-264-1399
    +1-909-992-0619
    Toll Free : +1-877-853-6098
  • +1-909-992-3401
Images
Western Blot (Tissue lysate)
Application

Western Blot (Tissue lysate)

GUSB MaxPab polyclonal antibody. Western Blot analysis of GUSB expression in human liver.

Western Blot (Transfected lysate)
Application

Western Blot (Transfected lysate)

Western Blot analysis of GUSB expression in transfected 293T cell line (H00002990-T01) by GUSB MaxPab polyclonal antibody.

Lane 1: GUSB transfected lysate(71.61 KDa).
Lane 2: Non-transfected lysate.

  • Specification

    Product Description

    Mouse polyclonal antibody raised against a full-length human GUSB protein.MaxPab Polyclonal Antibody,MaxPab Polyclonal Antibodies,MaxPab,DNA Immune,DNA Immunization,Immune Technology

    Immunogen

    GUSB (NP_000172.1, 1 a.a. ~ 651 a.a) full-length human protein.

    Sequence

    MARGSAVAWAALGPLLWGCALGLQGGMLYPQESPSRECKELDGLWSFRADFSDNRRRGFEEQWYRRPLWESGPTVDMPVPSSFNDISQDWRLRHFVGWVWYEREVILPERWTQDLRTRVVLRIGSAHSYAIVWVNGVDTLEHEGGYLPFEADISNLVQVGPLPSRLRITIAINNTLTPTTLPPGTIQYLTDTSKYPKGYFVQNTYFDFFNYAGLQRSVLLYTTPTTYIDDITVTTSVEQDSGLVNYQISVKGSNLFKLEVRLLDAENKVVANGTGTQGQLKVPGVSLWWPYLMHERPAYLYSLEVQLTAQTSLGPVSDFYTLPVGIRTVAVTKSQFLINGKPFYFHGVNKHEDADIRGKGFDWPLLVKDFNLLRWLGANAFRTSHYPYAEEVMQMCDRYGIVVIDECPGVGLALPQFFNNVSLHHHMQVMEEVVRRDKNHPAVVMWSVANEPASHLESAGYYLKMVIAHTKSLDPSRPVTFVSNSNYAADKGAPYVDVICLNSYYSWYHDYGHLELIQLQLATQFENWYKKYQKPIIQSEYGAETIAGFHQDPPLMFTEEYQKSLLEQYHLGLDQKRRKYVVGELIWNFADFMTEQSPTRVLGNKKGIFTRQRQPKSAAFLLRERYWKIANETRYPHSVAKSQCLENSPFT

    Host

    Mouse

    Reactivity

    Human

    Quality Control Testing

    Antibody reactive against mammalian transfected lysate.

    Storage Buffer

    In 1x PBS, pH 7.4

    Storage Instruction

    Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

  • Applications

    Western Blot (Tissue lysate)

    GUSB MaxPab polyclonal antibody. Western Blot analysis of GUSB expression in human liver.

    Western Blot (Transfected lysate)

    Western Blot analysis of GUSB expression in transfected 293T cell line (H00002990-T01) by GUSB MaxPab polyclonal antibody.

    Lane 1: GUSB transfected lysate(71.61 KDa).
    Lane 2: Non-transfected lysate.
  • Gene Info — GUSB

    Entrez GeneID

    2990

    GeneBank Accession#

    NM_000181.1

    Protein Accession#

    NP_000172.1

    Gene Name

    GUSB

    Gene Alias

    FLJ39445, MPS7

    Gene Description

    glucuronidase, beta

    Omim ID

    253220 611499

    Gene Ontology

    Hyperlink

    Gene Summary

    The GUSB gene encodes beta-glucuronidase (EC 3.2.1.31), a lysosomal hydrolase involved in the stepwise degradation of glucuronic acid-containing glycosaminoglycans (Shipley et al., 1993 [PubMed 7680524]). It is a tetrameric glycoprotein composed of identical subunits (Oshima et al., 1987 [PubMed 3468507]). The GUSB gene is mutated in mucopolysaccharidosis type VII (MPS7; MIM 253220).[supplied by OMIM

    Other Designations

    -

  • Interactome
  • Pathway
  • Disease
Contact Info
  • +1-909-264-1399
    +1-909-992-0619
    Toll Free : +1-877-853-6098
  • +1-909-992-3401
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