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- Home > Products > Monoclonal Ab > Human > Binding > Others > GBA monoclonal antibody (M03), clone 2H4
GBA monoclonal antibody (M03), clone 2H4
- 目录号 # : H00002629-M03
- 访问频率 :
- 尺寸
- 价格
- 库存
- 可得性
- 购物车
- 100 ug
- USD $ 319
- order now, ship next day
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Phone : +886-2-87511888
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- Specification
- Product Description:
- Mouse monoclonal antibody raised against a partial recombinant GBA.
- Immunogen:
- GBA (NP_000148, 146 a.a. ~ 235 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.
- Sequence:
- SYFSEEGIGYNIIRVPMASCDFSIRTYTYADTPDDFQLHNFSLPEEDTKLKIPLIHRALQLAQRPVSLLASPWTSPTWLKTNGAVNGKGS
- Host:
- Mouse
- Reactivity:
- Human
- Isotype:
- IgG1 Kappa
- Quality Control Testing:
- Antibody Reactive Against Recombinant Protein.
Western Blot detection against Immunogen (35.64 KDa) .
- Storage Buffer:
- In 1x PBS, pH 7.2
- Storage Instruction:
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
- MSDS:
Download
- Applications
- Western Blot (Recombinant protein)
- Protocol Download
- Sandwich ELISA (Recombinant protein)
- Detection limit for recombinant GST tagged GBA is approximately 3ng/ml as a capture antibody.
- Protocol Download
- Application Image
- Western Blot (Recombinant protein)
- Sandwich ELISA (Recombinant protein)
- enlarge
- ELISA
- Entrez GeneID:
- 2629
- GeneBank Accession#:
- NM_000157
- Protein Accession#:
- NP_000148
- Gene Name:
- GBA
- Gene Alias:
- GBA1,GCB,GLUC
- Gene Description:
- glucosidase, beta; acid (includes glucosylceramidase)
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants encoding the same protein. [provided by RefSeq
- Other Designations:
- D-glucosyl-N-acylsphingosine glucohydrolase,OTTHUMP00000033992,OTTHUMP00000033993,glucocerebrosidase,glucocerebrosidase (alt.),lysosomal glucocerebrosidase
- Related Disease
- Alzheimer Disease
- Alzheimer disease
- Bone Diseases, Metabolic
- Cardiovascular Diseases
- Cognition Disorders
- Cystic fibrosis
- Deafness
- Dementia
- Diabetes Mellitus, Type 2
- Disease Progression
- Edema
- Epilepsy
- Essential Tremor
- Essential tremor
- Gaucher Disease
- Gaucher disease
- Genetic Diseases, Inborn
- Genetic Predisposition to Disease
- Hypergammaglobulinemia
